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Congenital Pouch Colon

  • Amulya K. SaxenaEmail author
  • Praveen Mathur
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Abstract

Congenital pouch colon (CPC) is a rare form of anorectal malformation, in which the entire colon is replaced by an enormously dilated pouch that communicates with a fistula to the genitourinary tract. CPC is a condition which comprises of a high form of anorectal malformation which is associated with large variations in the size of the dilatations of the affected colonic segment. Surgical management depends on the type of CPC, and outcomes are variable depending on the length of colon affected and the anorectal muscle complex.

Keywords

Congenital pouch colon Congenital malformation Pull-through procedure Protective colostomy Coloplasty 

Notes

Acknowledgments

Adapted with permission of Taylor and Francis.

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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of Pediatric SurgeryChelsea and Westminster Hospital NHS Foundation Trust, Imperial College LondonLondonUK
  2. 2.Department of Pediatric SurgerySMS Medical CollegeJaipurIndia

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