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Teratomas (All Locations)

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Pediatric Surgery

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Abstract

Teratomas are the most common form of germ cell tumors in children. Sacrococcygeal teratoma (SCT) is the most common teratoma presenting at birth. Fetuses with “high risk” SCT have a mortality rate of 40%–50%. While fetal surgery may benefit selected fetuses prior to 27 weeks gestation, many fetuses die due to consequences of rapid growth after 27 weeks. In the absence of fetal hydrops prior to 27 weeks or tumor rupture in utero, early delivery is associated with favorable outcomes. In the neonate with a large teratoma, life-threatening bleeding is a major complication during tumor excision. Laparoscopic median sacral artery division before SCT excision offers a safe approach to reduce the risk of major hemorrhage during surgery. As regards long-term outcomes, uncontrolled voiding, difficulty in bladder emptying, pyelonephritis, and constipation are more common in patients with SCT than in healthy children.

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Authors and Affiliations

  1. Children’s Health Ireland at Crumlin, Dublin, Ireland

    Thambipillai Sri Paran

  2. The National Children’s Hospital, Dublin, Ireland

    Thambipillai Sri Paran

  3. Children’s Health Ireland at Temple Street, Dublin, Ireland

    David Coyle

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  1. Thambipillai Sri Paran
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  2. David Coyle
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Correspondence to Thambipillai Sri Paran .

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Editors and Affiliations

  1. Our Lady’s Children's Hospital, National Children’s Research Centre, Dublin, Ireland

    Prem Puri

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Paran, T.S., Coyle, D. (2020). Teratomas (All Locations). In: Puri, P. (eds) Pediatric Surgery. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-38482-0_145-1

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  • DOI: https://doi.org/10.1007/978-3-642-38482-0_145-1

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-38482-0

  • Online ISBN: 978-3-642-38482-0

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