Esophageal Atresia

  • Michael E. HöllwarthEmail author
  • Holger Till
Living reference work entry


Esophageal atresia is one of the most common life-threatening congenital malformations of the newborn baby. Today, survival rates are around 95% and mortality is related mainly to extreme prematurity or severe associated malformations, predominantly cardiac anomalies. Operative reconstruction of the continuity of the esophagus or replacement by other organs is the surgical option. A large variety of operative strategies have been elaborated and proposed in the past to achieve this goal. Most of the reports are retrospective and there is a definite need for multicenter prospective protocols to evaluate the methods and results. Long-term complications are strictures of the anastomotic region, esophageal, gastric reflux with esophagitis, and tracheomalacia. Despite these problems, the overall health-related quality in adult persons is good. However, long-term follow-up investigations into adulthood including esophageal endoscopy are indicated.


Esophageal atresia Associate malformations Replacement Anastomotic stricture Anastomotic fistula Recurrence Dysmotility Gastric reflux Tracheomalcia Follow-up 


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© Springer-Verlag GmbH Germany 2017

Authors and Affiliations

  1. 1.Department of Paediatric and Adolescent SurgeryMedical University of GrazGrazAustria

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