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Pediatric Surgery pp 1–20Cite as

Esophageal Atresia

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Abstract

Esophageal atresia is one of the most common life-threatening congenital malformations of the newborn baby. Today, survival rates are around 95% and mortality is related mainly to extreme prematurity or severe associated malformations, predominantly cardiac anomalies. Operative reconstruction of the continuity of the esophagus or replacement by other organs is the surgical option. A large variety of operative strategies have been elaborated and proposed in the past to achieve this goal. Most of the reports are retrospective and there is a definite need for multicenter prospective protocols to evaluate the methods and results. Long-term complications are strictures of the anastomotic region, esophageal, gastric reflux with esophagitis, and tracheomalacia. Despite these problems, the overall health-related quality in adult persons is good. However, long-term follow-up investigations into adulthood including esophageal endoscopy are indicated.

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Authors and Affiliations

  1. Department of Paediatric and Adolescent Surgery, Medical University of Graz, Auenbruggerplatz 34, A-8036, Graz, Austria

    Michael E. Höllwarth & Holger Till

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  1. Michael E. Höllwarth
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  2. Holger Till
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Correspondence to Michael E. Höllwarth .

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  1. Our Lady’s Children's Hospital, National Children’s Research Centre, Dublin, Ireland

    Prem Puri

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Höllwarth, M.E., Till, H. (2017). Esophageal Atresia. In: Puri, P. (eds) Pediatric Surgery. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-38482-0_48-1

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