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Malrotation

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Book cover Pediatric Surgery

Abstract

Intestinal malrotation comprises the spectrum of abnormalities of midgut development associated with abnormal rotation and/or fixation. Intestinal malrotation is characterized by the congenital abnormal positioning of the midgut, narrowing the dorsal mesenteric root and putting the bowel at risk of midgut volvulus. It is usually associated to the presence of peritoneal folds, the Ladd’s bands, which cross from the colon and cecum to the duodenum and liver and can cause duodenal obstruction.

Patients with intestinal malrotation can remain asymptomatic or may present with signs of acute bowel obstruction, such as colicky abdominal pain, abdominal distention, bilious vomiting, or shock. The surgical treatment is the Ladd’s procedure with derotation of the volvulus, division of the Ladd’s bands, widening of the small intestine’s mesentery, appendectomy, and correctional placement of the cecum and colon.

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Author information

Authors and Affiliations

  1. Neonatal and Pediatric Surgeon, Division of General and Thoracic Surgery, The Hospital for Sick Children, Toronto, Canada

    Augusto Zani

  2. Assistant Professor of Surgery, Department of Surgery, University of Toronto, Toronto, Canada

    Augusto Zani

  3. Division Head of General and Thoracic Surgery, The Hospital for Sick Children, Toronto, Canada

    Agostino Pierro

  4. Robert M. Filler Professor of Surgery, Department of Surgery, University of Toronto, Toronto, Canada

    Agostino Pierro

Authors
  1. Augusto Zani
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  2. Agostino Pierro
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Correspondence to Agostino Pierro .

Editor information

Editors and Affiliations

  1. Our Lady’s Children's Hospital, National Children’s Research Centre, Dublin, Ireland

    Prem Puri

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© 2017 Springer-Verlag GmbH Germany

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Zani, A., Pierro, A. (2017). Malrotation. In: Puri, P. (eds) Pediatric Surgery. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-38482-0_64-1

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  • DOI: https://doi.org/10.1007/978-3-642-38482-0_64-1

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-38482-0

  • Online ISBN: 978-3-642-38482-0

  • eBook Packages: Springer Reference MedicineReference Module Medicine

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