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Klinische Neurologie pp 1–17Cite as

Idiopathische Dystonien

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Zusammenfassung

Dystonien stellen ein breites Spektrum von zentralnervös bedingten Bewegungsstörungen dar. Sie sind durch anhaltende Muskelkontraktionen gekennzeichnet, die häufig abnorme Haltungen oder repetitive Bewegungen verursachen. Bei etwa 80 % der Patienten findet man keine Ursache für die Bewegungsstörung. Die Dystonie in ihren unterschiedlichen Formen stellt eine häufige neurologische Erkrankung dar, die einer effizienten Therapie zugänglich ist. Für die Mehrzahl der Patienten mit fokalen Dystonien stellt Botulinumtoxin A die Therapie der Wahl dar. Die tiefe Hirnstimulation hat einen festen Stellenwert bei Patienten mit primär generalisierten Dystonien und wird auch in der Behandlung von weniger schwer betroffenen Patienten mit fokalen oder segmentalen Dystonien erwogen, wenn diese nicht gut auf die Therapie mit Botulinumtoxin ansprechen.

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Authors and Affiliations

  1. Neurologie und klinische Neurophysiologie, Schön Klinik München Schwabing, München, Deutschland

    Andrés Ceballos-Baumann

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  1. Andrés Ceballos-Baumann
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Correspondence to Andrés Ceballos-Baumann .

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Editors and Affiliations

  1. Essen, Germany

    Peter Berlit

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Ceballos-Baumann, A. (2018). Idiopathische Dystonien. In: Berlit, P. (eds) Klinische Neurologie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-44768-0_132-1

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  • DOI: https://doi.org/10.1007/978-3-662-44768-0_132-1

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-44768-0

  • Online ISBN: 978-3-662-44768-0

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