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Juvenile Xanthogranuloma

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The Uveitis Atlas

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Abstract

Juvenile xanthogranuloma is a non-Langerhans cell histiocytosis affecting young children. Although primarily a cutaneous disorder, it can affect the eye and its ocular manifestations are diverse. Involvement of the iris, choroid, conjunctiva, eyelid, and orbit have been described. Although typically a benign, self-limited disorder of the skin, ocular involvement can lead to vision-threatening complications, including hyphema, secondary glaucoma, and amblyopia. The clinician must be aware of this uncommon masquerade syndrome as prompt diagnosis and treatment are critical to prevent vision loss.

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Authors and Affiliations

  1. Cleveland Clinic Foundation, 9500 Euclid Avenue, Desk i-13, Cleveland, OH, 44109, USA

    Angela Bessette

  2. Department of Ophthalmic Oncology, Cole Eye Institute, Cleveland Clinic Foundation, 9500 Euclid Avenue, Desk i-329, Cleveland, OH, 44195, USA

    Arun Singh

  3. Cleveland Clinic Foundation, 9500 Euclid Avenue, Desk i-329, Cleveland, OH, 44195, USA

    Francesco Pichi

Authors
  1. Angela Bessette
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  2. Francesco Pichi
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  3. Arun Singh
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Corresponding author

Correspondence to Angela Bessette .

Editor information

Editors and Affiliations

  1. Advanced Eye Center, PGIMER, Chandigarh, India

    Vishali Gupta

  2. Ophthalmology, University of Nebraska Medical Center, Omaha, Nebraska, USA

    Quan Dong Nguyen

  3. Department of Ophthalmology, Pitié-Salpêtrière University, Paris, France

    Phuc LeHoang

  4. University of Lausanne, Lausanne, Switzerland

    Carl P Herbort Jr.

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© 2016 Springer India

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Bessette, A., Pichi, F., Singh, A. (2016). Juvenile Xanthogranuloma. In: Gupta, V., Nguyen, Q., LeHoang, P., Herbort Jr., C. (eds) The Uveitis Atlas. Springer, New Delhi. https://doi.org/10.1007/978-81-322-2506-5_126-1

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  • DOI: https://doi.org/10.1007/978-81-322-2506-5_126-1

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  • Publisher Name: Springer, New Delhi

  • Online ISBN: 978-81-322-2506-5

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